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KMID : 0358920050320020256
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Journal of the Korean Academy of Pedodontics
2005 Volume.32 No. 2 p.256 ~ p.261
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LOCALIZED SCLERODERMA IN A CHILD CASE REPORT
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Kim Eun-Young
Kim Jong-Soo
Yoo Seung-Hoon
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Abstract
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Scleroderma is a connective tissue disease of unknown etiology, but known as a kind of auto-immune disease. It is most common in women especially in 30∼50 years, and very rare in childhood.
It can be classified into two main classes: localized scleroderma & systemic sclerosis: Localized type has better prognosis, and usually involves skin only, or in some cases, the muscle below, except inner organs. Systemic type involves skin, oral mucosa and major internal organs.
Involving facial skin, we can see small and sharp nose, expressionless stare and narrow oral aperture. Usually they have Raynaud’s phenomenon, and in progress, show mouth opening limitation and sclerosis of tongue and gingiva. It is called CREST syndrome showing calcinosis cutis, Raynaud’s phenomenon, esophageal dysfunction, sclerodactyly, and telangioectasia.
Treatment of scleroderma is systemic and localized steroid therapy, use of collagen-link inhibitor (D-penicillamine), immune depressor and etc. Mouth opening limitation can be improved by mouth stretching exercise.
We report a 6 years old boy, diagnosed with localized scleroderma who had mouth opening limitation. We could get additional mouth opening, and have done successful restorative treatment of mandibular and maxillary 1st and 2nd deciduous molar under deep sedation with nitrous oxide and enflurane.
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KEYWORD
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Scleroderma, Mouth opening limitation, Nitrous oxide
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